MyBioSource.com's PMPCA Antibody is a Rabbit Polyclonal antibody. This antibody has been shown to work in applications such as: Western Blot. The PMPCA Antibody was generated using peptidase, mitochondrial processing subunit alpha, and PMPCA as the antigen and it reacts with Human, Mouse, and Rat.
Description
The protein encoded by this gene is found in the mitochondrion, where it represents the alpha subunit of a proteolytic heterodimer. This heterodimer is responsible for cleaving the transit peptide from nuclear-encoded mitochondrial proteins. Defects in this gene are a cause of spinocerebellar ataxia, autosomal recessive 2